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Table 1 The characteristic of these OT-DSD patients

From: Evaluation and treatment for ovotesticular disorder of sex development (OT-DSD) - experience based on a Chinese series

No

Karyotype

Prader grade

MR imaging

T post HCG (ng/dl)

L gonand

R gonad

L duct

R duct

UVB (cm)

Uterus

Gender assignment

Complication

Position

Tissue

Position

Tissue

1

46,XX

III

+

367.5

Ing

OT

Ing

OT

Tube

Tube

3.5/4.5/2.5

+

M

No

2

46,XY

III

-

213.3

Abd

OT

Abd

OT

Tube

Tube

2/5/4

-

M

S

3

46,XX/46,XY

II

+

379.9

Abd

O

Ing

OT

Tube

Tube

3.5/5/4.5

+

M

No

4

46,XX

IV

-

416.2

Scr

OT

Abd

O

Tube

Tube

4/6/3

+

M

No

5

46,XX

III

+

209.1

Ing

OT

Ing

OT

Tube

Tube

2.5/4.5/3.5

+

M

F

6

46,XX

III

+

541.1

Scr

OT

Scr

T

Tube

Vas

1.5/6.5/5.5

+

M

No

7

46,XX

III

+

254.4

Scr

OT

Scr

T

Tube

Vas

1/6.5/5

+

M

No

8

46,XX/46,XY

III

-

322.6

Scr

OT

Abd

O

Vas

Tube

2/5.5/4.5

+

U → M

No

9

46,XX/47,XXY

III

-

186.4

Ing

T

Abd

OT

Vas

Tube

2.5/4.5/3.5

+

M

No

10

46,XX

II

+

462.8

Scr

OT

Scr

OT

Vas

Vas

2.5/5/4

+

M

No

11

46,XX/46,XY

III

-

275.4

Ing

OT

Ing

OT

Tube

Tube

3/5.5/4

+

M

a

12

46,XX

II

+

302.2

Abd

O

Scr

T

Tube

Vas

3.5/6/3.5

+

M

a

13

46,XX

III

-

166.3

Abd

O

Ing

OT

Tube

Tube

1/5.5/5.5

+

F → M

a

14

46,XX

III

+

532.6

Scr

OT

Scr

OT

Tube

Vas

2/5/4.5

+

M

a

15

46,XX

II

+

178.6

Abd

O

Scr

OT

Tube

Tube

3/5/3.5

+

M → F

No

16

46,XX

V

-

346.2

Scr

OT

Scr

OT

Vas

Vas

5/4/3.5

-

M

a

  1. MR Müllerian remnant, L Left, R Right, UVB Length of urogenital sinus/ water-filled vagina/ the location of the vaginal confluence to the bladder neck, Ing Inguinal cana, Abd Abdominal cavity, Scr Scrotum, OT Ovotestis, O Ovary, T Testicle, Tube Fallopian tube, Vas Vas deferens, M Male, F Female, U Undetermined sex, F Fistula, S Urethral stricture, aDidn’t finished the second stage