From: Aphallia - congenital absence of the penis: a systematic review
Affected System | Organ | Anomaly | Reported | Result |
---|---|---|---|---|
Genitourinary | Renal | Ā | 63% (n:26) | Ā |
Ā | Renal Agenesis | Ā | 12% (n:5) | |
Ā | Hypoplastic renal | Ā | 4% (n:2) | |
Ā | Dysplastic renal | Ā | 19% (n:8) | |
Ā | Hydronephrosis | Ā | 34% (n:14) | |
Ureteral | Ā | 29% (n:12) | Ā | |
Ā | Reflux Ureteral | Ā | 26% (n:11) | |
Ā | Absence | Ā | 7% (n:3) | |
Ā | Ectopic Ureteral | Ā | 2% (n:1) | |
Ā | Ureterocele | Ā | 2% (n:1) | |
Bladder | Ā | 21% (n:9) | Ā | |
Ā | Absence of bladder | Ā | 7% (n:3) | |
Ā | Hypoplastic bladder | Ā | 4% (n:2) | |
Ā | Posterior bladder diverticulum | Ā | 4% (n:2) | |
Ā | Hemibladder | Ā | 2% (n:1) | |
Ā | Three bladders | Ā | 2% (n:1) | |
Prostate | Ā | 4% (n:2) | Ā | |
Ā | Prostate absence | Ā | 2% (n:1) | |
Ā | Hypoplastic prostate | Ā | 2% (n:1) | |
Urethra | Ā | 21% (n:9) | Ā | |
Ā | Absence of urethra | Ā | 9% (n:4) | |
Ā | Posterior ureteral valve | Ā | 7% (n:3) | |
Ā | Urethral stone | Ā | 2% (n:1) | |
Ā | Urethral stenosis | Ā | 4% (n:2) | |
Fistula | Ā | 80% (n: 28) | Ā | |
Ā | Urethrorectal | Ā | 46% (n:19) | |
Ā | Urethroperineal | Ā | 17% (n:7) | |
Ā | Vesicorectal | Ā | 59% (n:4) | |
Ā | Urachal fistula | Ā | 4% (n: 2) | |
Ā | Ureterorectal | Ā | 2% (n: 1) | |
Respiratory system | Lung | Ā | 9% (n:4) | Ā |
Ā | right lung absent | Ā | 2% (n:1) | |
Ā | pulmonary hypoplasia | Ā | 2% (n:1) | |
Ā | pulmonary hypertension | Ā | 2% (n:1) | |
Ā | pulmonary hyperplasia | Ā | 2% (n:1) | |
Cardiovascular system | Cardiac | Ā | 12% (n:5) | Ā |
Ā | PDA | Ā | 4% (n:2) | |
Ā | ASD | Ā | 4% (n:2) | |
Ā | tricuspid valve insufficiency | Ā | 7% (n:3) | |
Ā | hypertrophic myocardia | Ā | 2% (n:1) | |
Digestive system | Ā | Ā | 8% (n:3) | Ā |
Ā | Omphalocele | Ā | 4% (n:2) | |
Ā | duplicated colon, | Ā | 2% (n:1) | |
Ā | Duplicated caecum | Ā | 2% (n:1) | |
Ā | Duplicated appendix | Ā | 2% (n:1) | |
Ā | short bowel syndrome | Ā | 2% (n:1) | |
Musculoskeletal System | Lower Extremity | Ā | 4% (n:2) | Ā |
Ā | clubfoot bilateral | Ā | 4% (n:2) |